Synonyms MCCA; 3-methylcrotonyl-CoA carboxylase 1; 3-methylcrotonyl-CoA carboxylase biotin-containing subunit; 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha; MCCase subunit alpha; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
Accession IDs HS01269 (MetaCyc)
Q96RQ3 (UniProt)
Length 84362 bp
Map Position
[183,588,732 <- 183,673,093]
Location mitochondrial lumen
Reaction 6.4.1.4: 3-methylcrotonyl-CoA + hydrogen carbonate + ATP → 3-methylglutaconyl-CoA + ADP + phosphate + H+ (catalyzed by complex)
Pathway L-leucine degradation I